Vasculitis nke obere capillaries

Vasculitis nke obere capillaries

Vasculitis nke obere capillaries  

Nke a bụ nnukwu ìgwè nke vasculitis nke mgbidi arterioles, venules ma ọ bụ capillaries, prognosis nke na-agbanwe agbanwe na-adabere ma ọ dị ọcha ma ọ bụ systemic cutaneous vasculitis.

Ihe na-emekarị n'ụlọ ọgwụ bụ purpura (ntụpọ na-acha odo odo nke na-adịghị agwụ mgbe a na-agbanye ya) na-agbapụta ma na-abanye n'ime ya, karịsịa na akụkụ ụkwụ dị ala, na-emewanyewanye site na iguzo ọtọ, nke nwere ike iwe ọtụtụ ụdị (petechial na ecchymotic, necrotic , pustular ...) ma ọ bụ livedo. na-akpụ ụdị ntupu purplish (livedo reticularis) ma ọ bụ mottling (livedo racemosa) n'ụkwụ. Anyị nwekwara ike ịhụ ihe omume Raynaud (mkpịsị aka ole na ole na-acha ọcha na oyi).

Purpura na livedo nwere ike jikọta ya na ọnyá ndị ọzọ na akpụkpọ ahụ (papules, nodules, necrotic lesions, na-agba ọbara ọbara), urticaria na-edozi ahụ nke na-adịghị agwụ agwụ.

Ọnụnọ nke ngosipụta n'èzí akpụkpọ ahụ bụ ihe kpatara ike ndọda, na-egosi ọnụnọ nke ntinye aka na akụkụ ahụ:

  • nkwonkwo mgbu,
  • afọ mgbu, stool ojii, nsogbu ngafe,
  • ọ bụ neuropathy
  • edema nke akụkụ ụkwụ ala,
  • Ọbara mgbali elu,
  • nsogbu iku ume, asthma, ụkwara ọbara…

Dọkịta ahụ na-edepụta nyocha ndị a na-achọ maka ihe kpatara na ihe ịrịba ama nke ịdị njọ: nyocha ọbara na ọnụ ọgụgụ ọbara ọbara, nyocha maka mbufụt, nyocha imeju na akụrụ, wdg, chọọ ọbara na stool na x-ray dị ka isi oku si dị. x-ray ngụgụ n'ime ihe isi ike iku ume, wdg).

Vasculitis na-ebute site na ọrịa:

  • nje bacteria: streptococcus, gram-adịghị mma cocci (gonococcus na meningococcus)
  • nje virus: ịba ọcha n'anya, mononucleosis na-efe efe, HIV, wdg.
  • parasitic: ịba…
  • fungal: Candida albicans…

Vasculitis jikọtara ya na ọrịa immunological

  • Ụdị II (mixed monoclonal) na III (polyclonal mixed) cryoglobulinemia, jikọtara ya na ọrịa autoimmune, ọrịa (karịsịa ịba ọcha n'anya C) ma ọ bụ ọrịa ọbara.
  • HypocomplementĂ©mie (Mac Duffie's urticarienne vascularite)
  • HyperglobulinĂ©mie (Waldenström's hyperglobulinĂ©mique purple)
  • Njikọta: lupus, ọrịa Gougerot-Sjögren, ọrịa ogbu na nkwonkwo.
  • Vasculitis nke ọrịa ọbara na malignancies
  • Ọrịa leukemia, lymphoma, myeloma, cancer
  • Vasculitis jikọtara ya na ANCA (ọgwụ mgbochi neutrophil cytoplasmic)   

Micro Poly Angéite ma ọ bụ MPA

Micropolyangiitis (MPA) bụ angeitis necrotizing sistemu nke akara ngosi ya yiri nke PAN.

Ejikọtara MPA na ANCA nke ụdị anti-myeloperoxidase (anti-MPO) na ọ na-ebutekarị glomerulonephritis na-aga n'ihu ngwa ngwa na ntinye aka akpa ume nke na-adịghị na PAN.

Ngwọta MPA maka PAN na-amalite site na ọgwụgwọ corticosteroid, mgbe ụfọdụ na-ejikọta ya na immunosuppressants (cyclophosphamide karịsịa)

Ọrịa Wegener

Wegener's granulomatosis bụ vasculitis mmalite nke a na-ejikarị ENT ma ọ bụ mgbaàmà iku ume (sinusitis, pneumopathy, wdg) na-eguzogide ọgwụgwọ ọgwụ nje.

Na oge gboo, itinye aka na ENT (pansinusitis na-ebibi ihe), akpa ume (parenchymal nodules) na gbasara akụrụ (crescent pauci-immune necrotizing glomerulonephritis) na-emepụta triad nke Wegener's granulomatosis.

Akpụkpọ ahụ akpụkpọ anụ-mucous na-emetụta ihe dịka 50% nke ndị ọrịa: purpura (ahịhịa na-acha odo odo nke na-adịghị apụ mgbe a na-pịa ya) na-agbapụta ma banye, papules, nodules subcutaneous, ọnya anụ ahụ, pustules, vesicles, hyperplastic gingivitis ...

ANCA bụ nchoputa na evolushọn ule maka Wegener's granulomatosis, na mgbasa cytoplasmic fluorescence (c-ANCA), finely granular na perinuclear nkwalite na / ma ọ bụ kpam kpam perinuclear fluorescence (p-ANCA).

Nlekọta nke granulomatosis nke Wegener, nke a na-ewere mgbe ụfọdụ dị ka ihe mberede ahụike, kwesịrị ime ya na ụlọ ọgwụ pụrụ iche, site na ngwakọta nke cortisone na cyclophosphamide ọnụ.

Churg na ọrịa Strauss

Asthma bụ isi na mmalite mmalite nke vasculitis a, nke ọ na-ebute na nkezi site na afọ 8 tupu akara mbụ nke vasculitis (neuropathy, sinus disorders, wdg) na nke na-aga n'ihu ma emesịa.

Nnwale ọbara na-egosi karịsịa mmụba doro anya na mkpụrụ ndụ ọbara ọcha eosinophilic polynuclear

Ọgwụgwọ nke ọrịa Churg na Strauss na-amalite site na ọgwụgwọ corticosteroid, mgbe ụfọdụ na-ejikọta ya na immunosuppressants (karịsịa cyclophosphamide).

Echiche dọkịta anyị    

Purpura infiltrated (ọcha acha odo odo, nke na-adịghị ada n'ime mkpịsị aka) bụ isi ihe ịrịba ama nke vasculitis.

N'ụzọ dị mwute, ihe ịrịba ama a anaghị adị mgbe niile na mgbanwe nke akara ngosi ahụike na-akọwaghị na-emekarị ka nchọpụta ahụ sie ike maka ndị dọkịta.

N'otu aka ahụ, ọ na-esikarị ike ịchọta ihe kpatara ọgwụgwọ na obere arịa vasculitis, nke bụ ihe kachasị mkpa na-ezute na omume ugbu a ma e jiri ya tụnyere ọkara na nnukwu vasculitis: ihe dị ka ọkara nke obere vasculitis arịa. arịa enweghị ihe kpatara achọpụtara n'oge nyocha nke ndu na redio nke dọkịta na-eme iji chọọ etiology. Anyị na-ekwukarị maka "vasculitis nfụkasị" ma ọ bụ "vasculitis hypersensitivity" ma ọ bụ kama " vasculitis akpụkpọ anụ nke obere arịa idiopathic caliber ".

Dr. Ludovic Rousseau, onye na -ahụ maka akpụkpọ ahụ

 

akara

Otu Ọmụmụ Vasculitis French: www.vascularites.org

Dermatonet.com, saịtị ozi na akpụkpọ ahụ, ntutu na ịma mma nke onye na -ahụ maka akpụkpọ ahụ

MedicineNet: http://www.medicinenet.com/vasculitis/article.htm

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