Nri na cystic fibrosis

General nkọwa nke ọrịa

Cystic fibrosis bụ ọrịa mkpụrụ ndụ ihe nketa na-emetụta imeju, bronchi, pancreas, salivary, genital, ọsụsọ, eriri afọ, glands (ya bụ, ọ na-emetụta akụkụ ahụ mucous). Nke a na-akọwa kpọmkwem aha ọrịa ahụ. Ọ sụgharịrị site na Latin dị ka " imi" na "oke, viscous."

Ihe na-akpata cystic fibrosis bụ mkpụrụ ndụ mutated a na-akpọ transmembrane regulator ma ọ bụ mkpụrụ ndụ cystic fibrosis. Ọ bụ ya na-ahụ maka mmepụta protein nke na-achịkwa mmegharị nke chlorine na akpụkpọ ahụ, yana akụkụ ahụ mmadụ dum. N'ime ndị nwere cystic fibrosis, mkpụrụ ndụ ihe nketa a anaghị arụ ọrụ ya nke ọma, nke na-eduga n'ihe nzuzo na-ekwekọghị n'okike (ọsụsọ na-aghọ nnu nnu, akpụkpọ ahụ mucous na-aghọ nke na-arapara na viscous).

Ụdị cystic fibrosis na mgbaàmà ha

1. Bronchopulmonary cystic fibrosis. Ọ na-eme na 20% nke ikpe, maka ụdị a - njirimara na-adịgide adịgide, ụkwara na-egbuke egbuke, na-egbu mgbu, na-enwekarị ọgụ, ebe sputum adịghị adịkarị na ikewapụ. N'ime oge nke oke - oyi baa, bronchitis. Usoro nke ọrịa ndị a siri ike na ogologo oge. Okpomọkụ ahụ na-ebili na ogo 38.5-39, mkpụmkpụ ume na-apụta.

2. eriri afọ cystic fibrosis dara na 5% nke ndị bi na ya. Isi atụmatụ nke ụdị ọrịa a:

  • ụbara agụụ, ma n'otu oge ahụ enweghi oke ahụ na-ahụ anya na anya ọtọ;
  • mmegharị afọ ugboro ugboro;
  • bloating na flatulence na-adịgide adịgide;
  • nnukwu mgbu afọ.

3. Ngwakọta cystic fibrosis na-emekarị (75%). A na-akpọkwa ya pulmonary. Ngosipụta nwere ike ịbụ na ngwakọta nke ụdị nke mbụ na nke abụọ nke cystic fibrosis.

Ọtụtụ mgbe, cystic fibrosis na-egosipụta onwe ya na ụbọchị mbụ nke ndụ. N'otu oge ahụ, nwatakịrị ahụ na-enwe mmetụta gag mgbe nile, ọ dịghị stool, tummy na-azakarị. N'ụbọchị nke 12, nwatakịrị ahụ nwere akpụkpọ anụ na-acha uhie uhie na akọrọ, a na-ahụ arịa n'afọ. Ya onwe ya na-agwụ ike na ihe mgbaàmà nke ịṅụbiga mmanya ókè na-apụtawanye ìhè.

Ọzọkwa, ihe ka ọtụtụ n'ime ụmụaka nwere ọrịa "nwa nnu", mgbe a na-ahụ kristal nnu na ihu ma ọ bụ ogwe aka nke nwatakịrị ahụ, akpụkpọ ahụ nwere uto nnu. Ọrịa a nwere ike ịnọrọ onwe ya n'ụdị cystic fibrosis.

Nri bara uru maka cystic fibrosis

Site na ọrịa a, onye ọrịa kwesịrị iri nri mgbe ọ bụla o kwere mee ma na-eri ọtụtụ kalori na vitamin na-agbaze abụba dị ka o kwere mee: A, D, E, F, K (vitamin ndị a anaghị etinye uche na ndị ọrịa, yabụ, dose ahụ. nke oriri ha kwesịrị ịba ụba).

A na-ahụ vitamin ndị a niile dị mkpa na nri ndị dị otú ahụ:

1. Mmalite anụmanụ:

  • Mmiri ara ehi;
  • akwa nkochi ime akwa;
  • umeji;
  • caviar;
  • bọta;
  • azụ na mmanụ azụ (karịsịa mmanụ oké osimiri: salmon, squid, mackerel, sardines, eel, mackerel, tuna, trout, bara uru: azụ asa, pike perch);
  • anụ (karịsịa anụ ezi, beef, nwa atụrụ).

2. Ebe osisi si:

  • akwụkwọ nri (karọt, ose dị ụtọ ma na-ekpo ọkụ, kabeeji ọ bụla, tomato, cucumbers, ugu);
  • elu (pasili, dil, letus, galik, akwụkwọ ndụ akwụkwọ ndụ na eyịm, nettle, celery, sọrel, rhubarb, akwụkwọ nri);
  • mkpụrụ osisi na tomato (unere, apụl, pears, ash ugwu, apricots, piich, melons, persimmons, sea buckthorn, viburnum, currants, avocados);
  • ero;
  • mmanụ: ọka, sunflower, olive, aku, soybean, ugu, aku, linseed;
  • mkpụrụ osisi a mịrị amị: aprịkọt a mịrị amị, prunes, mịrị;
  • mkpụrụ, mkpụrụ (ahụekere, walnuts, pistachios, cashews, hazelnuts, almọnd), sesame;
  • ọka: ọka wit, oatmeal, buckwheat, ọka bali;
  • puo ọka wit;
  • nnu (iji mejupụta ihe furu efu, karịsịa na ọrịa "nwa nnu").

Iji zere afọ ntachi, ị ga-aṅụ ọtụtụ mmiri (ọ dịkarịa ala 2 lita mmiri kwa ụbọchị, na mgbakwunye na ihe ọṅụṅụ, compotes, decoctions).

Ọgwụ ọdịnala maka cystic fibrosis

Ojiji nke ogwu ogwu kwesiri ekewa n'ime otu di iche iche, dabere na ihe mgbaàmà.

  1. 1 Iji meziwanye nkewa nke sputum na bronchopulmonary cystic fibrosis, decoctions nke marshmallow, mullein, coltsfoot epupụta ga-enyere aka.
  2. 2 Iji normalize ọrụ nke pancreas na mgbochi eriri afọ, infusions nke dandelion, wheatgrass ma ọ bụ elecampane nwere mmetụta bara uru;
  3. 3 Iji gbochie ọrịa, ị chọrọ calendula, birch buds, na eucalyptus.
  4. 4 Iji kwalite ọgụ, dị ka ihe na-ewusi ike, mpụta nke radiola rosea na Eleutherococcus ga-enyere aka.

Na mgbakwunye na decoctions na infusions, a pụrụ ime inhalation na mmanụ dị mkpa (lavender, hyssop, citral, basil).

Nri dị ize ndụ ma na-emerụ ahụ maka cystic fibrosis

Enweghị ihe mgbochi pụrụ iche, naanị ị ga-ezere nri ndị nwere obere kalori, ma ọ bụghị na ahụ nwere ike imebi (ọ gaghị enwe ike ịmepụta ike zuru oke maka ndụ nkịtị).

N'ezie, ịkwesịrị ibi ndụ dị mma ma na-eri nri mgbe niile na n'ụzọ ziri ezi (na-enweghị nri dị mma, nri ngwa ngwa na nri ngwa ngwa).

Akwụsịla oke shuga ma ọ bụrụ na enweghị ọrịa shuga mellitus.

Ige nti!

Gọọmentị anaghị ahụ maka mbọ ọ bụla iji ozi ahụ enyere, yana anaghị ekwe gị nkwa na ọ gaghị emerụ gị ahụ n'onwe gị. Enweghị ike iji ihe ndị ahụ kọwaa ọgwụgwọ ma mee nchoputa. Gaa dọkịta gị mgbe niile!

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