ọdịnaya
- Lemp: gịnị bụ leukoencephalopathy multifocal na -aga n'ihu?
- Kedu ihe bụ leukoencephalopathy multifocal na-aga n'ihu?
- Kedu ihe bụ ihe na-akpata leukoencephalopathy multifocal na-aga n'ihu?
- Kedu ihe mgbaàmà nke leukoencephalopathy multifocal na-aga n'ihu?
- Kedu ka esi eme nchọpụta nke leukoencephalopathy multifocal na-aga n'ihu?
- Kedu ọgwụgwọ maka leukoencephalopathy multifocal na-aga n'ihu?
Lemp: gịnị bụ leukoencephalopathy multifocal na -aga n'ihu?
Ihe akaebe nke mgbanwe na ihe ọcha nke gbara gburugburu neurons, multifocal leukoencephalopathy na-aga n'ihu bụ ọrịa akwara ozi nke na-emetụta ọtụtụ mpaghara ụbụrụ n'otu oge ma jiri nwayọọ nwayọọ na-aga n'ihu. Ihe kpatara ya dị ọtụtụ.
Kedu ihe bụ leukoencephalopathy multifocal na-aga n'ihu?
Neurons (sel akwara dị na ụbụrụ) na-agbatị eriri akwara, nke a na-akpọ axon, nke ga-ejikọta na ndị ọzọ na ụbụrụ site na synapses (njedebe nke axon). Ihe irighiri akwara ndị a bụ n'ọbọ (myelin) nke na-ekewapụ ha na ibe ha ma bụrụ akụkụ nke ihe ọcha nke ụbụrụ.
Multifocal leukoencephalopathy (PML) na-aga n'ihu na-agba akaebe maka mgbanwe n'ọtụtụ ebe ụbụrụ nke n'ọbọ a nke gbara gburugburu axon, na-eme ka obere sekit dị n'etiti ha. Sekit ndị a dị mkpirikpi dị na mmalite nke dysfunctions nke ụbụrụ n'ihe gbasara nchịkọta nke uru ahụ, nke ọrụ ụbụrụ (echiche ma ọ bụ cognition) na nke akwara akwara nke uche. N'ihi ya, ọnọdụ ahụ mkpọnwụ, ọgba aghara nke echiche na uche.
Ọrịa akwara na-emebi emebi na-aga n'ihu na-aga n'ihu na-aga n'ihu na-aga n'ihu ma ọ bụ jiri nwayọ nwayọ ma na-emetụta ọtụtụ saịtị nke ụbụrụ (multifocal). Ihe kpatara ya dị ọtụtụ na mgbaàmà ya dabere na saịtị ndị emetụtara.
Kedu ihe bụ ihe na-akpata leukoencephalopathy multifocal na-aga n'ihu?
Ihe na-akpata leukoencephalopathy na-aga n'ihu na-aga n'ihu (PML) dị ọtụtụ ma dị iche iche na ọdịdị:
Ihe nketa ma ọ bụ mkpụrụ ndụ ihe nketa
Mgbe ụfọdụ na-amalite nnọọ n'isi dị ka ụfọdụ syndromes ma ọ bụ ọrịa ndị dị ka ọrịa Cadasil jikọtara a mkpụrụ ndụ ihe nketa mutation, Childhood Ataxia syndrome na mmalite nke cavities na ọcha okwu nke ụbụrụ site na mbibi nke myelin, multiple sclerosis (MS) nke na-eme na ihe nketa na mgbe ụfọdụ na-ebute cavities (ụdị cavitary MS), ma ọ bụ ọrịa ụbụrụ na-emebi emebi dị ka ọrịa X na-emebi emebi ma ọ bụ ọrịa mitochondrial.
Mmalite akwara
Ọ bụ mgbaka vaskụla nke kpatara mmebi nke obere arịa ụbụrụ (microangiopathy), metụtara afọ, ọbara mgbali elu ma ọ bụ ọrịa shuga na-adịghị mma.
Nke nsi sitere
Site n'ịṅụ ọgwụ ụfọdụ dị ka methotrexate eji agwọ ọrịa ụfọdụ ọrịa cancer ma ọ bụ ọrịa autoimmune (ọrịa ogbu na nkwonkwo ma ọ bụ RA, wdg), nsị nitric oxide (ọkụ na gas na-adịghị mma) ma ọ bụ iku ume heroin vapors (iji riri ahụ). Usoro ọgwụgwọ radieshon nwekwara ike gbanwee ihe ọcha dị n'ụbụrụ.
Nke degenerative si malite
Ejikọtara ya na usoro mkpali na-emetụta usoro ụjọ ahụ dị ka MS, leucoaraiosis, ma ọ bụ ọrịa Alzheimer, mgbe ụfọdụ sitere na ihe nketa ma ọ bụghị mgbe niile, na ọrịa ikpeazụ nke nchịkọta nke nkwụnye ego ga-akpaghasị nnyefe neuronal ( nkwụnye ego amyloid na neurofibrillary degeneration metụtara ọnụnọ nke protein na ụbụrụ, beta-amyloid peptide na protein tau).
Ọrịa na -efe efe
Ọ na-adịkarịghị na nje virus dị ka papillomavirus (virus JC) ma ọ bụ AIDS (2 ruo 4% nke HIV + ndị mmadụ).
Kedu ihe mgbaàmà nke leukoencephalopathy multifocal na-aga n'ihu?
Mgbaàmà nke leukoencephalopathy multifocal na-aga n'ihu (PML) dịgasị iche dabere na mpaghara emetụtara yana ihe kpatara usoro mmebi a na ụbụrụ:
- inwe mmetụta adịghị ike, ike ikwu okwu ma ọ bụ iche echiche na mmalite nke ọrịa;
- ịma jijiji na-ama ụma (ọrịa cerebellar) na ọgba aghara gait na ọrịa X na-emebi emebi ma ọ bụ ọrịa mitochondrial, nsogbu nke nhazi afọ ofufo, akara ngosi na-egosipụta n'isi mmalite nke usoro ihe nketa ma ọ bụ mkpụrụ ndụ ihe nketa na-aga n'ihu nke nta nke nta na enweghị atụ…;
- ọrịa psychiatric n'oge degeneration nke vaskụla si malite, na-emekarị mgbe e mesịrị na ndị agadi na ọnọdụ ọnọdụ, cognitive ọrịa (nwa oge-spatial disorientation, ebe nchekwa nsogbu), mgbe ụfọdụ delusions na mgbagwoju anya;
- enwe mmetụta uche na moto nkà na degenerations nke nsi si malite;
- mbelata ọgụgụ isi na mmebi ụbụrụ dị ka ọrịa Alzheimer na ebe nchekwa na-adịghị mma, nghazi, nlebara anya, nhazi nsogbu, nhazi na nhazi, iche echiche;
- ihe ize ndụ nke ihe mberede cerebrovascular (strok) na-abawanye na multifocal leukoencephalopathy na-aga n'ihu;
- migraines na epileptic ọdịdọ.
Kedu ka esi eme nchọpụta nke leukoencephalopathy multifocal na-aga n'ihu?
Ihe ịrịba ama ụlọ ọgwụ na-egosilarị ọrịa a, ma ọ ga-abụ ụbụrụ ụbụrụ dị ka Magnetic Resonance Imaging (MRI) nke ga-eme ka o kwe omume ịchọta ọnya na-egosi ihe ọcha nke ụbụrụ.
A na-egosipụta nchọta nje virus JC site na nkwụsị lumbar mgbe ụfọdụ ma ọ bụrụ na a na-enyo enyo nke leukoencephalopathy na-aga n'ihu nke multifocal leukoencephalopathy nke malitere.
A na-emekarị nchọpụta ọrịa AIDS ma ọ bụrụ na ọ bụghị, ekwesịrị nyocha ya.
Kedu ọgwụgwọ maka leukoencephalopathy multifocal na-aga n'ihu?
Ọgwụgwọ nke leukoencephalopathy multifocal na-aga n'ihu bụ nke kpatara ya:
- ịchọ ihe na-egbu egbu (ọgwụ, heroin, wdg) ma kpochapụ ha;
- nkwenye nke nchoputa nke ụbụrụ ụbụrụ maka ọrịa Alzheimer, MS, leukoaraiosis, dementia nke vaskụla si malite.
Ọnya nke ihe na-acha ọcha ga-anọgide na-enweghị ike ịgbagha na nkwado psychosocial na mkpali uche ga-ebelata ọganihu nke ọrịa a nke na-amalite mgbe ụfọdụ ruo ọtụtụ afọ.